BACKGROUND: Tuberous sclerosis complex (TSC) is an autosomal dominant disorder. It is characterized by seizures, mental retardation and hamartomatous lesions, including facial angiofibroma, subependymal giant cell astrocytoma, cardiac rhabdomyoma and renal angiomyolipoma (AML). AMLs can bleed severely in the retroperitoneal space. CASE PRESENTATION: Herein, we present the case of a TSC patient presenting with recurrent severe episodes of retroperitoneal hemorrhage from AMLs successfully managed by angio-embolization. CONCLUSION: Transarterial embolization is effective in preventing and controlling hemorrhage in patients with AMLs of the kidney.

Recurrent retroperitoneal hemorrhage in a patient with tuberous sclerosis complex: a case report

CHIARUGI, MASSIMO;
2008

Abstract

BACKGROUND: Tuberous sclerosis complex (TSC) is an autosomal dominant disorder. It is characterized by seizures, mental retardation and hamartomatous lesions, including facial angiofibroma, subependymal giant cell astrocytoma, cardiac rhabdomyoma and renal angiomyolipoma (AML). AMLs can bleed severely in the retroperitoneal space. CASE PRESENTATION: Herein, we present the case of a TSC patient presenting with recurrent severe episodes of retroperitoneal hemorrhage from AMLs successfully managed by angio-embolization. CONCLUSION: Transarterial embolization is effective in preventing and controlling hemorrhage in patients with AMLs of the kidney.
Chiarugi, Massimo; Martino, Mc; Pucciarelli, M; Decanini, L; Vignali, C.
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Utilizza questo identificativo per citare o creare un link a questo documento: http://hdl.handle.net/11568/125259
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